Currarino Syndrome and the Effect of a Large Anterior Sacral Meningocele on Distal Colostogram in an Anorectal Malformation

J Radiol Case Rep. 2016 Jun 30;10(6):16-21. doi: 10.3941/jrcr.v10i6.2068. eCollection 2016 Jun.

Abstract

Currarino syndrome is a congenital disorder, consisting of a triad of anomalies including an anorectal malformation, sacral anomaly, and a presacral mass. Anterior sacral meningoceles are the most common presacral mass. A young child presented to our institution with an unrepaired anorectal malformation and a large anterior sacral meningocele. We describe how the anterior meningocele affected the imaging work-up.

Keywords: Currarino triad; MRI; anorectal malformation; colostogram; meningocele.

Publication types

  • Case Reports

MeSH terms

  • Anal Canal / abnormalities*
  • Anal Canal / diagnostic imaging
  • Anal Canal / surgery
  • Anorectal Malformations / diagnostic imaging*
  • Anorectal Malformations / surgery
  • Contrast Media
  • Digestive System Abnormalities / diagnostic imaging*
  • Digestive System Abnormalities / surgery
  • Humans
  • Infant
  • Magnetic Resonance Imaging / methods*
  • Male
  • Meningocele / diagnostic imaging*
  • Meningocele / surgery
  • Rectum / abnormalities*
  • Rectum / diagnostic imaging
  • Rectum / surgery
  • Sacrum / abnormalities*
  • Sacrum / diagnostic imaging
  • Sacrum / surgery
  • Syringomyelia / diagnostic imaging*
  • Syringomyelia / surgery
  • Triiodobenzoic Acids

Substances

  • Contrast Media
  • Triiodobenzoic Acids
  • iodixanol

Supplementary concepts

  • Currarino triad